Recent insights in Pyrin inflammasome activation : identifying potential novel therapeutic approaches in Pyrin-associated autoinflammatory syndromes

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Journal of clinical immunology - ISSN 0271-9142-44:1 (2024) p. 1-13
Auteur(s)
    Flore Wouters, Jeroen Bogie, Andy Wullaert, Jeroen van der Hilst

Myeloid OTULIN deficiency couples RIPK3-dependent cell death to Nlrp3 inflammasome activation and IL-1β secretion

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Science immunology - ISSN 2470-9468-8:89 (2023) p.
Auteur(s)
    M. Giulia Doglio, Lien Verboom, Emily Ruilova Sosoranga, Ulrika C. Frising, Tomoko Asaoka, Yannick Gansemans, Filip Van Nieuwerburgh, Geert van Loo, Andy Wullaert

The autoinflammation-associated $NLRC4^{V341A}$ mutation increases microbiota-independent IL-18 production but does not recapitulate human autoinflammatory symptoms in mice

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Frontiers in immunology - ISSN 1664-3224-14 (2023) p. 1-14
Auteur(s)
    Elien Eeckhout, Tomoko Asaoka, Hanne Van Gorp, Dieter Demon, Charlotte Girard-Guyonvarc'h, Vanessa Andries, Lars Vereecke, Cem Gabay, Mohamed Lamkanfi, Geert van Loo, Andy Wullaert

Protein citrullination and NET formation do not contribute to the pathology of A20/TNFAIP3 mutant mice

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Scientific reports - ISSN 2045-2322-13:1 (2023) p. 1-11
Auteur(s)
    Karel F.A. Van Damme, Pieter Hertens, Arne Martens, Elisabeth Gilis, Dario Priem, Inge Bruggeman, Amelie Fossoul, Jozefien Declercq, Helena Aegerter, Andy Wullaert, Tino Hochepied, Esther Hoste, Lieselotte Vande Walle, Mohamed Lamkanfi, Savvas N. Savvides, Dirk Elewaut, Bart N. Lambrecht, Geert van Loo

Complex regulation of alarmins S100A8/A9 and secretion via gasdermin D pores exacerbates autoinflammation in familial Mediterranean fever

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The journal of allergy and clinical immunology - ISSN 0091-6749-152:1 (2023) p. 230-243
Auteur(s)
    Selina K. Jorch, Annika McNally, Philipp Berger, Jonas Wolf, Kim Kaiser, Andrian Chetrusca Covash, Stefanie Robeck, Isabell Pastau, Olesja Fehler, Saskia-L. Jauch-Speer, Sven Hermann, Michael Schafers, Hanne Van Gorp, Apurva Kanneganti, Joke Dehoorne, Filomeen Haerynck, Federica Penco, Marco Gattorno, Jae Jin Chae, Paul Kubes, Mohamed Lamkanfi, Andy Wullaert, Markus Sperandio, Thomas Vogl, Johannes Roth, Judith Austermann